Where to buy pku formula

Store the DRY scoop in this can. Failure to follow these instructions could result in severe harm. Once prepared, product can spoil quickly. Do not use prepared product if it is unrefrigerated for more than a total of 2 hours.

After opening can, keep tightly covered, store in a dry area and use contents within 1 month. Do not freeze powder and avoid excessive heat. Slide 1 of 1. Phenyl Free 1 Metabolic Powder. What's the difference? Phenyl Free 1 Metabolic Powder 1. Select format. Select type. Select size. Change Location. Phenylketonuria PKU is a rare genetic disease caused by the inability of the body to metabolize the essential amino acid, phenylalanine Phe.

Left untreated, Phe will accumulate in the blood and body tissues and this excess Phe is toxic to the central nervous system. Untreated PKU will often lead to mental retardation, seizures and other serious medical conditions. PKU disease is typically diagnosed at birth through newborn screening. Standard treatment of PKU requires a strict, life long, adherence to a special diet, which is very low in phenylalanine.

Because phenylalanine is present in almost all natural protein sources, the diet is extremely challenging for patients, requiring the elimination of foods that contain protein. Natural protein sources are replaced in the PKU patient with synthetic free amino acid protein substitutes called "metabolic formula" or they are often referred to as "medical foods". These protein sources are consumed daily in place of natural proteins.

GMP is produced during the cheese making process and it is the only naturally occurring protein that does not contain Phe in its pure form. The natural absence of Phe in this unique protein makes it ideal for the PKU diet. Glytactin was developed in collaboration with the University of Wisconsin and is a combination of GMP and certain critical amino acids, such as arginine and tyrosine, which are also not found naturally in GMP.

Use in conjunction with breast milk or infant formula as advised by a healthcare professional. The content you are trying to access is intended for Healthcare Professionals only. Are you a healthcare professional?

Enhancing Lives Together. Our Commitments Latest News. Phenylalanine may be present in trace amounts from other ingredients Download the PKU start datacard. Official Journal of the European Union, Adopted as a worldwide standard in Amendment: , , , , and Revision: EFSA Journal,